Neonatal severe haemophilia: A case report

نویسندگان

چکیده

Hemophilia A is an inherited bleeding disorder caused by deficiency of coagulation factor VIII. It transmitted in X-linked recessive pattern from female carriers to male children. We report the observation a severe hemophilia newborn with history siblings who present hemarthrosis left elbow. The diagnosis was suspected and confirmed through biologic investigations imaging. Therefore, patient put under VIII good evolution. congenital hemorrhagic disease related anti-hemophilic factor. severity syndrome correlated level. There are three varieties hemophilia: severe, moderate minor. main complications hemarthrosis, hematomas variable location externalized hemorrhages. favorable prognosis depends on rapid diagnosis, monitoring immediate medical treatment. Diagnosis should be rule out all newborns family hemophilia, presence cord at birth or during circumcision.

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ژورنال

عنوان ژورنال: World Journal of Biology Pharmacy and Health Sciences

سال: 2023

ISSN: ['2582-5542']

DOI: https://doi.org/10.30574/wjbphs.2023.14.1.0186